Pathology paivs is the combination of obstruction of the pulmonary outflow tract from pulmona. Paivs involves complete blockage of the pulmonary valve located on the right side of the heart. Valvulotomia pulmonar percutanea mediante radiofrecuencia en. Atresia pulmonar con comun icacion interventricular gustavo a.
The valve is completely closed thereby obstructing the outflow of blood from the heart to the lungs. Percutaneous management of pulmonary atresia with intact. Caracteristicas morfologicas angiograficas na atresia. Gabriel cassalet bustillo, md atresia pulmonar con septo interventricular integro manuel r. Atresia pulmonar con septum interventricular integro. Atresia pulmonar con septo interventricular intacto y. Perforacion y valvuloplastia pulmonar mediante tecnica mecanica modificada.
In a normal functioning heart, the opening to the pulmonary valve has. Pulmonary atresia with intact ventricular septum percutaneous. Atresia pulmonar con septo integro connecting repositories. Jun 02, 2011 pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration. Pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration. In patients with pulmonary atresia with intact ventricular septum paivs, radiofrequencyassisted perforation of the valve is the most widely used initial therapy. Pulmonary atresia with an intact ventricular septum. Su reparacion requiere multiples operaciones y cateterismos. Pulmonary atresia is a congenital malformation of the pulmonary valve in which the valve orifice fails to develop. Atresia pulmonar con septo integro bive ntricular uno y medio glenn univentricular fontan figura 3. Pulmonary atresia with intact interventricular septum. Congenital heart defects facts about pulmonary atresia cdc. The influence of ventricular morphology and coronary artery dominance and morphology on early mortality in patients with pulmonary atresia and intact ventricular septum.
Atresia pulmonar con tabique interventricular integro en una cardiopata congnita ciantica con flujo pulmonar disminuido y cardiomegalia. A single uniform approach in the management of this disease is. Atresia pulmonar con comunicacion interventricular cirugia. Atresia pulmonar con tabique interventricular integro. Atresia pulmonar con septum interventricular intacto. Atresia pulmonar con comunicacion interventricular apciv. Atresia pulmonar com comunicacao interventricular cardio. Houston methodist debakey cv education 2,7 views 12. Atresia pulmonar con septum interventricular intacto scielo cuba.
This blockage prevents the flow of blood to the lungs. Pulmonary atresia with intact ventricular septum paivs and critical pulmonary stenosis cps are rare forms of cyanotic congenital heart disease 1,2 where pulmonary blood flow depends on the ductus arteriosus. Pdf atresia pulmonar con septo integro researchgate. Pulmonary atresia with intact ventricular septum paivs is a rare congenital malformation. The pulmonary valve is located on the right side of the heart between the right ventricle and pulmonary artery. Atresia pulmonar com septo integroatresia pulmonar com septo integro definicao. Pulmonary atresia with intact ventricular septum and critical pulmonary stenosis in newborns encompasses a wide spectrum of disease, including cases with significant right ventricular hypoplasia and coronary artery to right ventricle fistulae, which may be considered a contraindication for decompression of the right ventricle. Atresia pulmonar con septo integro cirugia cardiovascular. Atresia pulmonar con septo integro francisco portela, sonia marcos cirugia cardiaca infantil y cardiologia infantil complejo hospitalario juan canalejo. In this form of pulmonary atresia, the wall, or septum, between the ventricles remains complete and intact. During pregnancy when the heart is developing, very little blood flows into or out of the right ventricle rv, and therefore the rv doesnt fully develop and remains very small. Pulmonary atresia with intact ventricular septum paivs is a relatively uncommon form of congenital heart disease and is remarkable in its morphologic diversity, characterized by varying degrees of right ventricle rv hypoplasia and associated with tricuspid valve dysplasia and sinusoidal right ventriculocoronary connections.
Pdf pulmonary atresia with intact ventricular septum is an apparently simple cyanotic congenital heart disease. Atresia pulmonar con septo integro asociada a estenosis aortica. Atresia pulmonar con septo integro article pdf available in cirugia cardiovascular 212 april 2014 with 43 reads how we measure reads. Pulmonary atresia with intact interventricular septum paivs is a subtype of pulmonary atresia that presents as cyanotic congenital heart disease. Atresia pulmonar con septo integro biventricular 60% fontan 24% uno y medio 12% paliacion 3% trasplante 1% figura 4.
47 144 926 624 982 700 856 919 116 287 910 1076 144 166 559 1082 1002 1169 1206 680 1508 1235 1333 543 848 69 1445 1157 520 434